Cranial MRI in Acute Hyperammonemic Encephalopathy

被引：25

作者：

Bindu, Parayil S. ^{[1
]}

Sinha, Sanjib ^{[1
]}

Taly, Arun B. ^{[1
]}

Christopher, Rita ^{[2
]}

Kovoor, Jerry M. E. ^{[3
]}

机构：

[1] Natl Inst Mental Hlth & Neurosci, Dept Neurol, Bangalore 560029, Karnataka, India

[2] Natl Inst Mental Hlth & Neurosci, Dept Neurochem, Bangalore 560029, Karnataka, India

[3] Natl Inst Mental Hlth & Neurosci, Dept Neuroimaging & Intervent Radiol, Bangalore 560029, Karnataka, India

来源：

PEDIATRIC NEUROLOGY | 2009年 / 41卷 / 02期

关键词：

ORNITHINE TRANSCARBAMYLASE DEFICIENCY; UREA CYCLE DISORDERS; CITRULLINEMIA;

D O I：

10.1016/j.pediatrneurol.2009.02.012

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Cranial magnetic resonance imaging was performed in three cases of acute hyperammonemic encephalopathy with three diverse etiologies: infantile citrullinemia, acute hepatic encephalopathy, and proximal urea cycle disorder. All three patients exhibited diffuse extensive cortical signal changes and swelling. Neurologic outcome was poor in all three cases. Knowledge of the magnetic resonance imaging findings of hyperammonemic encephalopathy may help in early diagnosis and treatment and could influence the neurologic outcome. (C) 2009 by Elsevier Inc. All rights reserved.

引用

页码：139 / 142

页数：4

共 13 条

[1] Albayram S, 2002, AM J NEURORADIOL, V23, P334
[2] Acute hepatic encephalopathy with diffuse cortical lesions
Arnold, SM
Els, T
Spreer, J
Schumacher, M
[J]. NEURORADIOLOGY, 2001, 43 (07) : 551 - 554
[3] BAGANZ MD, 1994, AM J NEURORADIOL, V15, P1779
[4] Extensive cortical magnetic resonance signal change in proximal urea cycle disorder
Bindu, P. S.
Sinha, S.
Taly, A. B.
Chandrasekhar, H. S.
Christopher, R.
Arunodaya, G. R.
Shetty, T.
[J]. JOURNAL OF CHILD NEUROLOGY, 2007, 22 (02) : 238 - 239
[5] Brusilow SW., 2001, METABOLIC MOL BASES, P1909
[6] MRI in a case of adult-onset citrullinemia
Chen, YF
Huang, YC
Liu, HM
Hwu, WL
[J]. NEURORADIOLOGY, 2001, 43 (10) : 845 - 847
[7] Choi CG, 2001, AM J NEURORADIOL, V22, P834
[8] NEUROPATHOLOGY OF CITRULLINEMIA
MARTIN, JJ
FARRIAUX, JP
DE JONGHE, P
[J]. ACTA NEUROPATHOLOGICA, 1982, 56 (04) : 303 - 306
[9] NEUROLOGIC OUTCOME IN CHILDREN WITH INBORN-ERRORS OF UREA SYNTHESIS - OUTCOME OF UREA-CYCLE ENZYMOPATHIES
MSALL, M
BATSHAW, ML
SUSS, R
BRUSILOW, SW
MELLITS, ED
[J]. NEW ENGLAND JOURNAL OF MEDICINE, 1984, 310 (23) : 1500 - 1505
[10] Takanashi J, 2003, AM J NEURORADIOL, V24, P390

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