Idiopathic hypersomnia (IH) is characterized by excessive daytime sleepiness despite normal or prolonged sleep. IH is distinguished from narcolepsy by the female predominance, severe morning inertia, continuous drowsiness (rather than sleep attacks), unrefreshing naps, absence of cataplexy, sleep onset in REM periods, and hypocretin deficiency. In IH, the multiple sleep latency test demonstrates low sensitivity, specificity, and reproducibility, compared with prolonged sleep monitoring. In some IH cases, an endogenous hypnotic peptide stimulating GABA receptors during wakefulness is suspected, which are improved by anti-GABA drugs. The benefits of modafinil, sodium oxybate, mazindol, and pitolisant were found in mostly retrospective studies.
机构:
Grp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Univ Paris 06, CNRS UMR7225, UMRS975, Ctr Rech,Inst Cerveau & Moelle Epiniere, Paris, France
Inserm U975, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Lavault, Sophie
Dauvilliers, Yves
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Inserm U888, Montpellier, France
Hop Gui de Chauliac, Serv Neurol, Montpellier, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Dauvilliers, Yves
Drouot, Xavier
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Hop Henri Mondor, AP HP, Serv Physiol, F-94010 Creteil, France
Univ Paris 12, EA4391, Creteil, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Drouot, Xavier
Leu-Semenescu, Smaranda
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Grp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Leu-Semenescu, Smaranda
Golmard, Jean-Louis
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Univ Paris 06, CNRS UMR7225, UMRS975, Ctr Rech,Inst Cerveau & Moelle Epiniere, Paris, France
Grp Hosp Pitie Salpetriere, AP HP, Unite Biostat & Informat Med, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Golmard, Jean-Louis
Lecendreux, Michel
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机构:
CHU Robert Debre, AP HP, Ctr Pediat Pathol Sommeil, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Lecendreux, Michel
Franco, Patricia
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Hop Mere Couple Enfant, Hosp Civils Lyon, Unites Explorat Fonct Neurol, Lyon, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
机构:
Hop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Ctr Natl Reference Narcolepsie & Hypersomnie, Paris, FranceHop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Leu-Semenescu, Smaranda
Louis, Pauline
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h-index: 0
机构:
Hop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Univ Paris 06, Paris, FranceHop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
机构:
Natl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Hop La Pitie Salpetriere, AP HP, Serv Pathol Sommeil, F-75651 Paris 13, France
Univ Paris 06, Ctr Rech, Inst Cerveau & Moelle Epiniere, CNRS UMR7225,Inserm U1127, Paris, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Leu-Semenescu, Smaranda
Nittur, Nandy
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Hop La Pitie Salpetriere, AP HP, Serv Pathol Sommeil, F-75651 Paris 13, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Nittur, Nandy
Golmard, Jean-Louis
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h-index: 0
机构:
Univ Paris 06, Hop Univ Pitie Salpetriere, Dept Biostat, ER4, Paris, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
机构:
Grp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Univ Paris 06, CNRS UMR7225, UMRS975, Ctr Rech,Inst Cerveau & Moelle Epiniere, Paris, France
Inserm U975, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Lavault, Sophie
Dauvilliers, Yves
论文数: 0引用数: 0
h-index: 0
机构:
Inserm U888, Montpellier, France
Hop Gui de Chauliac, Serv Neurol, Montpellier, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Dauvilliers, Yves
Drouot, Xavier
论文数: 0引用数: 0
h-index: 0
机构:
Hop Henri Mondor, AP HP, Serv Physiol, F-94010 Creteil, France
Univ Paris 12, EA4391, Creteil, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Drouot, Xavier
Leu-Semenescu, Smaranda
论文数: 0引用数: 0
h-index: 0
机构:
Grp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Leu-Semenescu, Smaranda
Golmard, Jean-Louis
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 06, CNRS UMR7225, UMRS975, Ctr Rech,Inst Cerveau & Moelle Epiniere, Paris, France
Grp Hosp Pitie Salpetriere, AP HP, Unite Biostat & Informat Med, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Golmard, Jean-Louis
Lecendreux, Michel
论文数: 0引用数: 0
h-index: 0
机构:
CHU Robert Debre, AP HP, Ctr Pediat Pathol Sommeil, Paris, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
Lecendreux, Michel
Franco, Patricia
论文数: 0引用数: 0
h-index: 0
机构:
Hop Mere Couple Enfant, Hosp Civils Lyon, Unites Explorat Fonct Neurol, Lyon, FranceGrp Hosp Pitie Salpetriere, AP HP, Unite Pathol Sommeil, F-75634 Paris, France
机构:
Hop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Ctr Natl Reference Narcolepsie & Hypersomnie, Paris, FranceHop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Leu-Semenescu, Smaranda
Louis, Pauline
论文数: 0引用数: 0
h-index: 0
机构:
Hop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
Univ Paris 06, Paris, FranceHop Univ Pitie Salpetriere, AP HP, Serv Pathol Sommeil, Paris, France
机构:
Natl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Hop La Pitie Salpetriere, AP HP, Serv Pathol Sommeil, F-75651 Paris 13, France
Univ Paris 06, Ctr Rech, Inst Cerveau & Moelle Epiniere, CNRS UMR7225,Inserm U1127, Paris, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Leu-Semenescu, Smaranda
Nittur, Nandy
论文数: 0引用数: 0
h-index: 0
机构:
Hop La Pitie Salpetriere, AP HP, Serv Pathol Sommeil, F-75651 Paris 13, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France
Nittur, Nandy
Golmard, Jean-Louis
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 06, Hop Univ Pitie Salpetriere, Dept Biostat, ER4, Paris, FranceNatl Reference Ctr Narcolepsy & Idiopath Hypersom, Montpellier, France