Light chain deposition disease complicating familial Mediterranean fever

被引：2
作者：
Vella, JP
Doyle, GD
Campbell, E
Walshe, JJ
机构：
[1] BEAUMONT HOSP,DIV NEPHROL,DUBLIN 9,IRELAND
[2] BEAUMONT HOSP,DIV PATHOL,DUBLIN 9,IRELAND
来源：
AMERICAN JOURNAL OF KIDNEY DISEASES | 1997年 / 29卷 / 06期
关键词：
familial Mediterranean fever; light chain deposition disease; renal failure; chemotherapy; transplantation; AMYLOIDOSIS; MYELOMA;
D O I：
10.1016/S0272-6386(97)90470-4
中图分类号：
R5 [内科学]; R69 [泌尿科学（泌尿生殖系疾病）];
学科分类号：
1002 ; 100201 ;
摘要：
Familial Mediterranean fever (fMf) is an inherited condition characterized by polyserositis and is sometimes complicated by AA renal amyloidosis leading to nephrotic syndrome and renal failure. We present a case of a man with fMf who presented with rapidly progressive renal failure caused by light chain deposition disease. This disease association has not previously been described in the medical literature. (C) 1997 by the National Kidney Foundation, Inc.
引用
收藏
页码：942 / 946
页数：5
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