Plastic Bronchitis as an Unusual Cause of Mucus Plugging in Cystic Fibrosis

被引：19

作者：

Mateos-Corral, Dimas ^{[1
]}

Cutz, Ernest ^{[2
]}

Solomon, Melinda ^{[1
]}

Ratjen, Felix ^{[1
]}

机构：

[1] Hosp Sick Children, Div Resp Med, Toronto, ON M5G 1X8, Canada

[2] Hosp Sick Children, Pediat Lab Med, Toronto, ON M5G 1X8, Canada

来源：

PEDIATRIC PULMONOLOGY | 2009年 / 44卷 / 09期

关键词：

plastic bronchitis; cystic fibrosis; N-acetylcysteine; dornase alfa;

D O I：

10.1002/ppul.21063

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Cystic fibrosis patients are known to produce abundant, purulent sputum consisting mainly of DNA and cellular debris. We present a case of a CF patient with recurrent airway obstruction caused by a rare condition known as plastic bronchitis (PB). PB is characterized by the formation of casts of the airways that cause obstruction. Multiple etiologies have been proposed, but to our knowledge, no CF patient has been reported in any PB classification. Histological analysis and in-vitro testing of the cast were important factors in choosing the adequate therapy in this patient. Pediatr Pulmonol. 2009; 44:939-940. (C) 2009 Wiey-Liss, Inc.

引用

页码：939 / 940

页数：2

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