Endoscopic Decompression for Optic Neuropathy in McCune-Albright Syndrome

被引：1

作者：

Noh, Jung-Hoon ^{[1
]}

Kong, Doo-Sik ^{[1
]}

Seol, Ho Jun ^{[1
]}

Shin, Hyung Jin ^{[1
]}

机构：

[1] Sungkyunkwan Univ, Sch Med, Samsung Med Ctr, Dept Neurosurg, Seoul 135710, South Korea

来源：

JOURNAL OF KOREAN NEUROSURGICAL SOCIETY | 2014年 / 56卷 / 03期

关键词：

Fibrous dysplasia; McCune-Albright syndrome; Acromegaly; PITUITARY-ADENOMA; PROTEIN;

D O I：

10.3340/jkns.2014.56.3.281

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

McCune-Albright syndrome (MAS) is characterized by a triad of poly/monostotic fibrous dysplasia, cafe-au-lait macules and hyperfunctioning endocrinopathies including human growth hormone excess. Acromegaly as a manifestation of endocrine hyperfunction with MAS is uncommon. Surgical excision may be challenging due to the associated severe fibrous dysplasia of the skull base. Through the endoscopic procedures, we treated a case of MAS presenting with compressive optic neuropathy due to fibrous dysplasia and acromegaly caused by growth hormone secreting pituitary adenoma. We reviewed the literature on GH excess in MAS to highlight its surgical and medical challenges.

引用

页码：281 / 283

页数：3

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