Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus

被引:29
|
作者
Cohen, D [1 ]
Kutluay, E [1 ]
Edwards, J [1 ]
Peltier, A [1 ]
Beydoun, A [1 ]
机构
[1] Univ Michigan, Hlth Syst, Dept Neurol, Ann Arbor, MI 48109 USA
关键词
Creutzfeldt-Jakob disease; status epilepticus; Wernicke's aphasia;
D O I
10.1016/j.yebeh.2004.06.019
中图分类号
B84 [心理学]; C [社会科学总论]; Q98 [人类学];
学科分类号
03 ; 0303 ; 030303 ; 04 ; 0402 ;
摘要
Creutzfeldt-Jakob disease (CJD) is a rare prion disease characterized by a spongiform encephalopathy in humans. Although the characteristic triad of myoclonus, dementia, and periodic EEG activity is easy to recognize, unusual manifestations of the disease may be challenging and create a diagnostic dilemma. We report a case of CJD that occurred in a 26-year-old patient who presented with a receptive (Wernicke's) aphasia secondary to nonconvulsive status epilepticus. (C) 2004 Elsevier Inc. All rights reserved.
引用
收藏
页码:792 / 796
页数:5
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