Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus

被引：30

作者：

Cohen, D ^{[1
]}

Kutluay, E ^{[1
]}

Edwards, J ^{[1
]}

Peltier, A ^{[1
]}

Beydoun, A ^{[1
]}

机构：

[1] Univ Michigan, Hlth Syst, Dept Neurol, Ann Arbor, MI 48109 USA

来源：

EPILEPSY & BEHAVIOR | 2004年 / 5卷 / 05期

关键词：

Creutzfeldt-Jakob disease; status epilepticus; Wernicke's aphasia;

D O I：

10.1016/j.yebeh.2004.06.019

中图分类号：

B84 [心理学]; C [社会科学总论]; Q98 [人类学];

学科分类号：

03 ; 0303 ; 030303 ; 04 ; 0402 ;

摘要：

Creutzfeldt-Jakob disease (CJD) is a rare prion disease characterized by a spongiform encephalopathy in humans. Although the characteristic triad of myoclonus, dementia, and periodic EEG activity is easy to recognize, unusual manifestations of the disease may be challenging and create a diagnostic dilemma. We report a case of CJD that occurred in a 26-year-old patient who presented with a receptive (Wernicke's) aphasia secondary to nonconvulsive status epilepticus. (C) 2004 Elsevier Inc. All rights reserved.

引用

页码：792 / 796

页数：5