Primary Renal Synovial Sarcoma

被引:0
|
作者
MacNevin, Wyatt [1 ]
Rendon, Ricardo A. [2 ]
Colwell, Bruce [3 ]
Wang, Cheng [2 ,4 ]
Hache, Kelly Dakin [4 ]
Merrimen, Jennifer [2 ,4 ]
Mason, Ross J. [2 ]
机构
[1] Dalhousie Univ, Fac Med, Halifax, NS, Canada
[2] Dalhousie Univ, Dept Urol, Fac Med, Halifax, NS, Canada
[3] Dalhousie Univ, Dept Med, Div Med Oncol, Fac Med, Halifax, NS, Canada
[4] Dalhousie Univ, Dept Pathol, Fac Med, Halifax, NS, Canada
来源
JOURNAL OF UROLOGICAL SURGERY | 2022年 / 9卷 / 03期
关键词
Synovial sarcoma; kidney neoplasm; SYT-SSX; SOFT-TISSUE SARCOMA;
D O I
10.4274/jus.galenos.2022.2021.0094
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Primary renal synovial sarcoma is a rare malignancy that may present similarly to other renal neoplasms. The diagnosis of synovial sarcoma is performed through the identification of a SYT-SSX gene fusion. Here, we present a case of a primary renal synovial sarcoma in a patient who presented with renal mass initially thought to be renal cell carcinoma until further pathological characterization. After undergoing radical open nephrectomy, the patient developed pulmonary and psoas metastases and was treated with systemic therapy.
引用
收藏
页码:221 / 224
页数:4
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