Nephrogenic fibrosing dermopathy in children

被引：40

作者：

Auron, Ari

Shao, Lei

Warady, Bradley A. ^{[1
]}

机构：

[1] Univ Missouri, Kansas City Sch Med, Sect Pediat Nephrol, Childrens Mercy Hosp, Kansas City, MO 64110 USA

[2] Univ Missouri, Kansas City Sch Med, Sect Pathol, Childrens Mercy Hosp, Kansas City, MO 64110 USA

来源：

PEDIATRIC NEPHROLOGY | 2006年 / 21卷 / 09期

关键词：

nephrogenic fibrosing dermopathy; pediatrics; nephrogenic systemic fibrosis; chronic kidney disease; dialysis; kidney transplant;

D O I：

10.1007/s00467-006-0174-7

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Nephrogenic fibrosing dermopathy (NFD) is an entity of unknown etiology that has only been reported in patients with impaired kidney function. It has characteristic diagnostic findings by skin biopsy and due to its systemic involvement in some reported cases, the term "nephrogenic systemic fibrosis" has been recently suggested as more appropriate for the nomenclature of this entity. There is no curative treatment currently available and very few cases have been reported in children. We hereby report two cases so as to alert pediatric health care providers about the existence of this disorder.

引用

页码：1307 / 1311

页数：5

共 25 条

[1] Nephrogenic fibrosing dermopathy after liver transplantation successfully treated with plasmapheresis [J].