Pulmonary Arterial Hypertension Associated with Congenital Heart Disease

被引：10

作者：

Krishnan, Usha ^{[1
]}

Rosenzweig, Erika B. ^{[1
]}

机构：

[1] Columbia Univ, Med Ctr, Pulm Hypertens Ctr, Div Pediat Cardiol, New York, NY 10032 USA

来源：

CLINICS IN CHEST MEDICINE | 2013年 / 34卷 / 04期

关键词：

Pulmonary arterial hypertension; Congenital heart disease; Eisenmenger syndrome; Operability; Fontan; PROTEIN-LOSING ENTEROPATHY; INHALED NITRIC-OXIDE; EISENMENGER-SYNDROME; LUNG-TRANSPLANTATION; VASCULAR-RESISTANCE; PLASTIC BRONCHITIS; BOSENTAN THERAPY; DOUBLE-BLIND; OPEN-LABEL; FONTAN;

D O I：

10.1016/j.ccm.2013.08.011

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

In the past decade, there have been more patients with congenital heart disease (CHD) surviving to adulthood; whether due to late repair, or complex underlying CHD, many of these patients will be faced with pulmonary arterial hypertension (PAH) associated with CHD (APAH-CHD). In this review, the authors discuss the most commonly encountered forms of APAH-CHD, how to interpret the hemodynamic data, and how to classify the patients into meaningful subgroups that have similar management strategies. The current state of targeted medical treatments available to patients with APAH-CHD is also discussed.

引用

页码：707 / +

页数：12

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