SURGICAL TREATMENT OF DEFORMITIES AND FRACTURES ON LOWER LIMBS WITH OSTEOGENESIS IMPERFECTA

Objective: To provide a review of patients with Osteogenesis Imperfecta by analyzing the deformities, fractures and results of surgical treatment on lower limbs in order to determine the efficiency of the use of non-elongating rods (non extensible). Materials and Method: Medical records, preoperative and postoperative X-ray images of all the patients who had imperfect osteogenesis and treated at the Alfred I duPont Institute (USA) between 1965 and 1999 have been reviewed. Results: Fourteen patients (five boys and nine girls) were submitted to the non-elongating rods on their lower limbs, totaling 37 procedures. Conclusion: The procedure of intramedullary fixation with non-elongating rods to treat fractures and deformities on lower limb in Osteogenesis Imperfecta was proven to be a low morbidity method without interfering with the ambulatory status of these patients.