Study Design. Retrospective study of posterior hemivertebra resection and osteotomies with transpedicular instrumentation in very young children. Objective. Assessment of early intervention in congenital scoliosis with almost complete correction of the main deformity. Summary of Background Data. There is a trend to early correction of congenital deformities, however, there is a lack of long-term follow-up. Methods. Forty-one children aged 1 to 6 years with congenital scoliosis were operated on by hemivertebra resection by a posterior only approach with transpedicular instrumentation. Mean age at time of surgery was 3 years 5 months. They were retrospectively studied with a mean follow-up of 6 years 2 months. Results. In group 1 (patients without bar formation), the average Cobb angle of the main curve was 36 before surgery and 7 after surgery. Compensatory cranial curve improved spontaneously from 15 to 3, compensatory caudal curve from 17 to 4. The angle of kyphosis was 22 before surgery and 8 after surgery. In group 2 (patients with bar formation) the main curve improved from 69 to 23, cranial curve from 27 to 11, caudal curve from 34 to 14, and kyphosis from 24 to 9. Conclusion. Posterior hemivertebra resection, in case of bar formation with osteotomy of the bar, allows for excellent correction in both the frontal and sagittal planes, with a short segment of fusion. Early surgery in young children prevents the development of severe local deformities and secondary structural curves, thus allowing for normal growth in the unaffected parts of the spine.