Treatment of scleromyxedema with 2-chlorodeoxyadenosine

被引:23
作者
Davis, LS [1 ]
Sanal, S [1 ]
Sangueza, OP [1 ]
机构
[1] MED COLL GEORGIA,DEPT PATHOL,AUGUSTA,GA 30912
关键词
D O I
10.1016/S0190-9622(96)90650-7
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Scleromyxedema is an unusual skin disease that is characterized by a proliferation of fibroblasts and an accumulation of mucin. Despite experience with multiple forms of therapy, no single agent has proved uniformly beneficial in this condition. We describe a patient with scleromyxedema who was treated successfully with 2-chlorodeoxyadenosine (2-CdA), a purine analog used mainly in the treatment of lymphoproliferative disorders.
引用
收藏
页码:288 / 290
页数:3
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