共 71 条
Pulmonary Hypertension in Congenital Heart Disease Beyond Eisenmenger Syndrome
被引:7
作者:

Krieger, Eric V.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Seattle Adult Congenital Heart Serv, Div Cardiol, Dept Med,Sch Med, Seattle, WA 98195 USA Univ Washington, Seattle Adult Congenital Heart Serv, Div Cardiol, Dept Med,Sch Med, Seattle, WA 98195 USA

Leary, Peter J.
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h-index: 0
机构:
Univ Washington, Pulm Vasc Dis Program, Div Pulm & Crit Care Med, Dept Med,Sch Med, Seattle, WA 98195 USA Univ Washington, Seattle Adult Congenital Heart Serv, Div Cardiol, Dept Med,Sch Med, Seattle, WA 98195 USA

Opotowsky, Alexander R.
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h-index: 0
机构:
Boston Childrens Hosp, Dept Cardiol, Boston Adult Congenital Heart & Pulm Hypertens Se, Boston, MA 02115 USA
Brigham & Womens Hosp, Boston, MA 02115 USA Univ Washington, Seattle Adult Congenital Heart Serv, Div Cardiol, Dept Med,Sch Med, Seattle, WA 98195 USA
机构:
[1] Univ Washington, Seattle Adult Congenital Heart Serv, Div Cardiol, Dept Med,Sch Med, Seattle, WA 98195 USA
[2] Univ Washington, Pulm Vasc Dis Program, Div Pulm & Crit Care Med, Dept Med,Sch Med, Seattle, WA 98195 USA
[3] Boston Childrens Hosp, Dept Cardiol, Boston Adult Congenital Heart & Pulm Hypertens Se, Boston, MA 02115 USA
[4] Brigham & Womens Hosp, Boston, MA 02115 USA
关键词:
Adult congenital heart disease;
Pulmonary hypertension;
Pulmonary arterial hypertension disease management;
Humans vasodilator agents/diagnostic use/therapeutic use;
ATRIAL SEPTAL-DEFECT;
INHALED NITRIC-OXIDE;
ARTERIAL-HYPERTENSION;
VASCULAR-RESISTANCE;
EXERCISE CAPACITY;
AMERICAN-COLLEGE;
POTTS SHUNT;
TASK-FORCE;
ADULT;
SILDENAFIL;
D O I:
10.1016/j.ccl.2015.07.003
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
Patients with adult congenital heart disease have an increased risk of developing pulmonary hypertension. There are several mechanisms of pulmonary hypertension in patients with adult congenital heart disease, and understanding them requires a systematic approach to define the patient's hennodynamics and physiology. This article reviews the updated classification of pulmonary hypertension in patients with adult congenital heart disease with a focus on pathophysiology, diagnostics, and the evaluation of pulmonary hypertension in special adult congenital heart disease populations.
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页码:599 / +
页数:12
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共 71 条
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