We report here the case of a 22-year-old female patient with an incomplete Ebstein's anomaly, complete heart block and atrial standstill. Atrial paralysis associated with Ebstein's anomaly is the most important feature, since there is a report of familial Ebstein's anomaly associated with atrial standstill but isolated cases have not been described. The patient presented with atypical chest pain and a symptomatic bradycardia of 37 beats per minute. A VVIR pacemaker was implanted. She has subsequently been symptom free. (C) 2002 The European Society of Cardiology. Published by Elsevier Science Ltd. All rights reserved.
机构:
Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Farre, Nuria
Bazan, Victor
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Bazan, Victor
Garcia-Garcia, Cosme
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Garcia-Garcia, Cosme
Recasens, Lluis
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Recasens, Lluis
Marti-Almor, Julio
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Marti-Almor, Julio
Ascoeta, Soledad
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Ascoeta, Soledad
Valles, Ermengol
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Valles, Ermengol
Merono-Duenas, Oona
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Merono-Duenas, Oona
Ribas, Nuria
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
Ribas, Nuria
Bruguera-Cortada, Jordi
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Univ Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, SpainUniv Autonoma Barcelona, Hosp del Mar, Dept Cardiol, E-08193 Barcelona, Spain
机构:
Med Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Med Coll Wisconsin, Dept Surg, Div Congenital Heart Surg, 8700 W Wisconsin Ave, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Thareja, Suma K.
Frommelt, Michele A.
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Childrens Wisconsin, Dept Pediat, Div Pediat Cardiol, Milwaukee, WI 53226 USA
Childrens Wisconsin, Herma Heart Inst, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Frommelt, Michele A.
Lincoln, Joy
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Childrens Wisconsin, Dept Pediat, Div Pediat Cardiol, Milwaukee, WI 53226 USA
Childrens Wisconsin, Herma Heart Inst, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Lincoln, Joy
Lough, John W.
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Med Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Lough, John W.
Mitchell, Michael E.
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Med Coll Wisconsin, Dept Surg, Div Congenital Heart Surg, 8700 W Wisconsin Ave, Milwaukee, WI 53226 USA
Childrens Wisconsin, Dept Pediat, Div Pediat Cardiol, Milwaukee, WI 53226 USA
Childrens Wisconsin, Herma Heart Inst, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
Mitchell, Michael E.
Tomita-Mitchell, Aoy
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Med Coll Wisconsin, Dept Surg, Div Congenital Heart Surg, 8700 W Wisconsin Ave, Milwaukee, WI 53226 USA
Childrens Wisconsin, Dept Pediat, Div Pediat Cardiol, Milwaukee, WI 53226 USA
Childrens Wisconsin, Herma Heart Inst, Milwaukee, WI 53226 USAMed Coll Wisconsin, Dept Cell Biol Neurobiol & Anat, Milwaukee, WI 53226 USA
机构:
Division of Cardiology, Department of Medicine, University of Stellenbosch, Cape TownDivision of Cardiology, Department of Medicine, University of Stellenbosch, Cape Town
John T.-J.
Snyman H.W.
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Division of Cardiology, Department of Medicine, University of Stellenbosch, Cape TownDivision of Cardiology, Department of Medicine, University of Stellenbosch, Cape Town
Snyman H.W.
Janson J.
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机构:
Department of Cardiothoracic Surgery, University of Stellenbosch, Cape TownDivision of Cardiology, Department of Medicine, University of Stellenbosch, Cape Town
Janson J.
Pecoraro A.J.K.
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机构:
Division of Cardiology, Department of Medicine, University of Stellenbosch, Cape TownDivision of Cardiology, Department of Medicine, University of Stellenbosch, Cape Town
机构:
Univ Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, IndonesiaUniv Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, Indonesia
Limbong, M.
Ardhianto, P.
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机构:
Univ Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, IndonesiaUniv Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, Indonesia
Ardhianto, P.
Herry, Y.
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Univ Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, IndonesiaUniv Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, Indonesia
Herry, Y.
Priyatno, A.
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Diponegoro Univ, Fac Med, Dr Kariadi Gen Hosp, Dept Paediat,Div Cardiol, Semarang, IndonesiaUniv Diponegoro, Fac Med, Dept Cardiol & Vasc Med, Semarang, Indonesia