Intimal sarcoma of the pulmonary artery: a differential diagnosis of chronic pulmonary thromboembolism

被引：12

作者：

Alves Valle Dornas, Ana Paula ^{[1
]}

Assis Figueiredo Campos, Frederico Thadeu ^{[2
]}

Rezende, Claudia Juliana ^{[3
]}

Ribeiro, Carlos Alberto ^{[4
]}

Amaral, Nilson Figueiredo ^{[5
]}

Correa, Ricardo de Amorim ^{[6
]}

机构：

[1] Fac Ciencias Med Minas Gerais, Ctr Pesquisa & Posgrad, Belo Horizonte, MG, Brazil

[2] Hosp Madre Teresa, Serv Pneumol, Belo Horizonte, MG, Brazil

[3] Hosp Madre Teresa, Ctr Diagnost Imagem, Belo Horizonte, MG, Brazil

[4] Hosp Madre Teresa, Inst Roberto Alvarenga, Belo Horizonte, MG, Brazil

[5] Hosp Madre Teresa, Serv Cirurgia Torac, Belo Horizonte, MG, Brazil

[6] Univ Fed Minas Gerais, Fac Med, Disciplina Pneumol, Belo Horizonte, MG, Brazil

来源：

JORNAL BRASILEIRO DE PNEUMOLOGIA | 2009年 / 35卷 / 08期

关键词：

Pulmonary embolism; Hypertension; pulmonary; Hemangiosarcoma; Diagnosis; differential; HYPERTENSION;

D O I：

10.1590/S1806-37132009000800015

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Intimal sarcoma of the pulmonary artery is a rare and potentially lethal tumor, the diagnosis of which is difficult and therefore frequently delayed. The clinical signs and symptoms are nonspecific, often mimicking chronic pulmonary thromboembolism (CPTE). We report the case of a 45-year-old male under treatment for CPTE associated with pulmonary arterial hypertension and chronic cor pulmonale. There was no response to treatment with anticoagulants and sildenafil. We emphasize the difficulties in diagnosing intimal sarcoma of the pulmonary artery, the need to investigate this neoplasm in the differential diagnosis of CPTE and the systematic use of criteria for the appropriate prescription of new medications for pulmonary artery hypertension.

引用

页码：814 / 818

页数：5

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