A patient with chronic inflammatory demyelinating polyneuropathy (CIDP) developed Evans syndrome (hemolytic anemia/thrombocytopenia) 17 months after onset of symptoms despite different immunomodulatory treatments. A therapeutic approach with the chimeric monoclonal anti-CD20 antibody rituximab induced substantial improvement of CIDP and hematologic recovery. The patient remains in sustained remission 17 months after completion of therapy. Rituximab may represent a successful therapy in otherwise refractory CIDP.
机构:
Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, EnglandGuys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Hughes, R
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Bensa, S
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Bensa, S
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Willison, H
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Willison, H
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Van den Bergh, P
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Van den Bergh, P
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Comi, G
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Comi, G
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Illa, I
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Illa, I
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Nobile-Orazio, E
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Nobile-Orazio, E
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van Doorn, P
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
van Doorn, P
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Dalakas, M
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Dalakas, M
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Bojar, M
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Bojar, M
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Swan, A
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
机构:
Guys Kings & St Thomas Sch Med, Dept Clin Neurosci, London SE1 1UL, EnglandGuys Kings & St Thomas Sch Med, Dept Clin Neurosci, London SE1 1UL, England
机构:
Cornell Univ, Weill Med Coll, Peripheral Neuropathy Ctr, New York, NY 10022 USACornell Univ, Weill Med Coll, Peripheral Neuropathy Ctr, New York, NY 10022 USA
机构:
Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, EnglandGuys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Hughes, R
;
Bensa, S
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Bensa, S
;
Willison, H
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机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Willison, H
;
Van den Bergh, P
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h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Van den Bergh, P
;
Comi, G
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Comi, G
;
Illa, I
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Illa, I
;
Nobile-Orazio, E
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Nobile-Orazio, E
;
van Doorn, P
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
van Doorn, P
;
Dalakas, M
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Dalakas, M
;
Bojar, M
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
Bojar, M
;
Swan, A
论文数: 0引用数: 0
h-index: 0
机构:Guys Kings & St Thomas Sch Med, Dept Neuroimmunol, Guys Hosp, London SE1 9RT, England
机构:
Guys Kings & St Thomas Sch Med, Dept Clin Neurosci, London SE1 1UL, EnglandGuys Kings & St Thomas Sch Med, Dept Clin Neurosci, London SE1 1UL, England
机构:
Cornell Univ, Weill Med Coll, Peripheral Neuropathy Ctr, New York, NY 10022 USACornell Univ, Weill Med Coll, Peripheral Neuropathy Ctr, New York, NY 10022 USA