An Interesting Case of Bilateral Upper Limb Wasting: Hirayama Disease

被引:0
作者
Eugin, Priscilla Rubavathy [1 ]
Chinnusamy, Manokaran [1 ]
Janakiraman, Sathiyanarayanan [1 ]
机构
[1] Sri Manakula Vinayagar Med Coll & Hosp, Dept Gen Med, Pondicherry, India
来源
JOURNAL OF HEALTH AND ALLIED SCIENCES NU | 2021年 / 11卷 / 01期
关键词
Hirayama disease; dynamic MRI; motor neuron disease; JUVENILE MUSCULAR-ATROPHY; DISTAL UPPER EXTREMITY;
D O I
10.1055/s-0040-1718237
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Hirayama disease is a rare neurologic disease and is characterized by insidious unilateral or bilateral muscular atrophy and weakness of the forearms and hands without sensory or pyramidal signs. Our patient presented with bilateral upper limb wasting, which is a rarer variant of motor neuron disease. The diagnosis of Hirayama disease is based on dynamic magnetic resonance imaging (MRI). This case displays how dynamic cervical spine MRI can pick up dynamic cord compression and contributes to zero in the diagnosis of Hirayama disease.
引用
收藏
页码:40 / 43
页数:4
相关论文
共 10 条
[1]  
[Anonymous], 1991, HDB CLIN NEUROLOGY
[2]  
Chen CJ, 1998, AM J NEURORADIOL, V19, P365
[3]   FOCAL CERVICAL POLIOPATHY CAUSING JUVENILE MUSCULAR-ATROPHY OF DISTAL UPPER EXTREMITY - A PATHOLOGICAL-STUDY [J].
HIRAYAMA, K ;
TOMONAGA, M ;
KITANO, K ;
YAMADA, T ;
KOJIMA, S ;
ARAI, K .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1987, 50 (03) :285-290
[4]  
Hirayama K, 1959, Psychiatr Neurol Jpn, V61, P2190
[5]   A Confirmed Case in the United Kingdom of Hirayama Disease in a Young White Male Presenting with Hand Weakness [J].
Lewis, Daniel ;
Saxena, Ankur ;
Herwadkar, Amit ;
Leach, John .
WORLD NEUROSURGERY, 2017, 105 :1039.e7-1039.e12
[6]   Central motor conduction in brachial monomelic amyotrophy [J].
Pal, Pramod K. ;
Atchayaram, Nalini ;
Goel, Gaurav ;
Beulah, Ebenezer .
NEUROLOGY INDIA, 2008, 56 (04) :438-443
[7]   Magnetic resonance imaging in juvenile asymmetric segmental spinal muscular atrophy [J].
Pradhan, S ;
Gupta, RK .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1997, 146 (02) :133-138
[8]   Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan [J].
Tashiro, K ;
Kikuchi, S ;
Itoyama, Y ;
Tokumaru, Y ;
Sobue, G ;
Mukai, E ;
Akiguchi, I ;
Nakashima, K ;
Kira, JI ;
Hirayama, K .
AMYOTROPHIC LATERAL SCLEROSIS AND OTHER MOTOR NEURON DISORDERS, 2006, 7 (01) :38-45
[9]  
Tokumaru Y, 2001, Rinsho Shinkeigaku, V41, P173
[10]   AMYOTROPHIC CERVICAL MYELOPATHY IN ADOLESCENCE [J].
TOMA, S ;
SHIOZAWA, Z .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1995, 58 (01) :56-64