Peutz-Jeghers Syndrome: A Circumventable Emergency

被引：6

作者：

Choudhury, Sourav ^{[1
]}

Das, Anupam ^{[3
]}

Misra, Priyankar ^{[4
]}

Ray, Udipta ^{[1
]}

Sarangi, Sujata ^{[2
]}

机构：

[1] Med Coll & Hosp, Dept Gen Surg, Kolkata, W Bengal, India

[2] Med Coll & Hosp, Dept Pathol, Kolkata, W Bengal, India

[3] KPC Med Coll & Hosp, Dept Dermatol, Kolkata, W Bengal, India

[4] Burdwan Med Coll & Hosp, Dept Dermatol, Kolkata, W Bengal, India

来源：

INDIAN JOURNAL OF DERMATOLOGY | 2018年 / 63卷 / 02期

关键词：

Colonic Mucosa-Associated Lymphoid Tissue Lymphoma; intussusception; Peutz-Jeghers syndrome; CANCER SYNDROMES; MALTOMA;

D O I：

10.4103/ijd.IJD_563_16

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Peutz-Jeghers syndrome (PJS) is characterized by multiple hamartomatous polyps in the gastrointestinal tract and mucocutaneous pigmentation. Here we present, a case of multiple gastrointestinal hamartomatous polyps in a 22-year-old male who had been operated for intestinal obstruction due to ileocolic intussusception. Resection of the affected segment was done with proximal ileostomy and distal mucous fistula formation. Clinicopathological diagnosis of PJS was made. Later, during ileostomy closure, it was found that the patient had a transverse colonic mass which was resected. Histological examination with immunohistochemistry confirmed it to be a Mucosa-Associated Lymphoid Tissue Lymphoma (MALToma). Colonic MALToma in the background of PJS is a unique case for which it has been reported.

引用

页码：168 / 171

页数：4

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