Uncooked cornstarch - Efficacy in type I glycogenosis

被引:19
作者
Lee, PJ
Dixon, MA
Leonard, JV
机构
[1] INST CHILD HLTH,MED UNIT,LONDON,ENGLAND
[2] GREAT ORMOND ST HOSP CHILDREN,DIETET DEPT,LONDON,ENGLAND
关键词
glycogen storage disease; uncooked cornstarch; glycaemic index;
D O I
10.1136/adc.74.6.546
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Uncooked cornstarch (UCCS) loads in 14 patients with type 1 glycogenosis revealed that satisfactory glycaemia was achieved for a median of 4.25 hours (range 2.5 to 6). Length of glycaemia was related weakly to UCCS dose, but not to patient age or measures of metabolic control. Careful. monitoring is required during UCCS treatment.
引用
收藏
页码:546 / 547
页数:2
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