Regional lymphomatoid papulosis: a report of four cases

被引:38
作者
Scarisbrick, JJ [1 ]
Evans, AV [1 ]
Woolford, AJ [1 ]
Black, MM [1 ]
Russell-Jones, R [1 ]
机构
[1] St Thomas Hosp, St Johns Inst Dermatol, Skin Tumour Unit, London SE1 7EH, England
关键词
lymphomatoid papulosis; regional distribution;
D O I
10.1046/j.1365-2133.1999.03218.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Lymphomatoid papulosis (LyP) is a chronic self-healing cutaneous eruption which is clinically benign but histologically malignant. Lesions occur episodically over the trunk and limbs. We describe four patients with regional LyP. All were male, with a range in age at onset from 12 to 47 years. In all cases, lesions were confined to a segmental unilateral area. Two patients had type A and two type B LyP. We have long-term follow-up on one patient whose lesions were limited to the right buttock for more than 20 years before more widespread lesions developed. Another patient with lesions on the left flank had mycosis fungoides limited to the same region. Only one other case of LyP presenting in a regional distribution has previously been described.
引用
收藏
页码:1125 / 1128
页数:4
相关论文
共 19 条
[1]   HOST RESPONSE IN LYMPHOMATOID PAPULOSIS [J].
AGNARSSON, BA ;
KADIN, ME .
HUMAN PATHOLOGY, 1989, 20 (08) :747-752
[2]  
Basarab T, 1998, BRIT J DERMATOL, V139, P630
[3]  
BELJAARDS RC, 1992, BRIT J DERMATOL, V126, P596
[4]  
CATTERALL MD, 1989, BR J DERMATOL S34, V121, P109
[5]   The same dominant T cell clone is present in multiple regressing skin lesions and associated T cell lymphomas of patients with lymphomatoid papulosis [J].
Chott, A ;
Vonderheid, EC ;
Olbricht, S ;
Miao, NN ;
Balk, SP ;
Kadin, ME .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1996, 106 (04) :696-700
[6]  
CLIFF S, 1996, CLIN EXP DERMATOL, V21, P461
[7]   LYMPHOMATOID PAPULOSIS - A CLINICAL AND HISTOPATHOLOGIC REVIEW OF 53 CASES WITH LEUKOCYTE IMMUNOPHENOTYPING, DNA FLOW-CYTOMETRY, AND T-CELL RECEPTOR GENE REARRANGEMENT STUDIES [J].
ELAZHARY, RA ;
GIBSON, LE ;
KURTIN, PJ ;
PITTELKOW, MR ;
MULLER, SA .
JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1994, 30 (02) :210-218
[8]   LOSS OF RECEPTORS FOR TRANSFORMING GROWTH-FACTOR-BETA IN HUMAN T-CELL MALIGNANCIES [J].
KADIN, ME ;
CAVAILLECOLL, MW ;
GERTZ, R ;
MASSAGUE, J ;
CHEIFETZ, S ;
GEORGE, D .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (13) :6002-6006
[9]   LYMPHOMATOID PAPULOSIS ASSOCIATED WITH PLAQUE-STAGE AND GRANULOMATOUS MYCOSIS-FUNGOIDES [J].
KARDASHIAN, JL ;
ZACKHEIM, HS ;
EGBERT, BM .
ARCHIVES OF DERMATOLOGY, 1985, 121 (09) :1175-1180
[10]   LYMPHOMATOID PAPULOSIS FOLLOWED BY LARGE-CELL LYMPHOMA - IMMUNOPHENOTYPICAL AND GENOTYPIC ANALYSIS [J].
KAUDEWITZ, P ;
HERBST, H ;
ANAGNOSTOPOULOS, I ;
ECKERT, F ;
BRAUNFALCO, O ;
STEIN, H .
BRITISH JOURNAL OF DERMATOLOGY, 1991, 124 (05) :465-469