Congenital long QT syndrome

被引:0
作者
Ahmed, Najeeb [1 ]
Riaz, Kamran [1 ]
Rai, Ripudeep [1 ]
Osman, Mohammed [1 ]
Wase, Abdul [1 ]
机构
[1] Wright State Univ, Boonshoft Sch Med, Dept Internal Med, Sect Electrophysiol,Good Samaritan Hosp, Dayton, OH 45435 USA
关键词
long QT syndrome; Torsade de Pointes; sudden cardiac death; Romano-Ward syndrome; Jervell and Lange-Nielsen syndrome;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Long QT syndrome (LQTS) can be asymptomatic-identifiable as an incidental finding on electrocardiogram-or it can present with palpitation, syncope, seizures, or sudden cardiac death. LQTS is characterized by a prolonged QT interval, which can be associated with a specific form of polymorphic ventricular tachycardia known as torsade de pointes. Other electrocardiogram changes in LQTS include T-wave abnormalities, particularly bifid T waves, U waves, and T-wave alternans. The precipitating factors of LQTS include electrolyte abnormalities, bradyarrhythmias, medications (such as antiarrhythmic drugs, antibiotics, antipsychotics, and antihistamines), and myocardial ischemia. The authors report a case of LQTS in a 47-year-old woman with no other significant cardiac history.
引用
收藏
页码:160 / 165
页数:6
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