Multicentric reticulohistiocytosis -: The long course of a rare disease

被引:9
作者
Blanco, JJR
Hernández, FJB
Cerezo, JG
García, IS
Rubio, FL
Rodríguez, JJV
机构
[1] Hosp Univ La Paz, Med Interna Serv, Madrid, Spain
[2] Hosp Univ La Paz, Serv Anat Patol, Madrid, Spain
关键词
multicentric reticulohistiocytosis; macrophages; cyclophosphamide;
D O I
10.1080/03009740252937658
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Multicentric reticulohistiocytosis is a rare systemic disease. The patients usually develop an erosive polyarthritis in a few years. The most effective treatment is still unclear due to the few reports published of this disease. We report a case of multicentric reticulohistiocytosis with clinical, histopathologic and immunohistochemical study. The patient was treated with cyclophosphamide and nonsteroidal antiinflammatory drugs with an infrequent long-term survival.
引用
收藏
页码:107 / 109
页数:3
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