Endovascular treatment of an unusual arterioportal fistula caused by the rupture of a giant hepatic artery aneurysm into the superior mesenteric vein in Behcet disease

BEHCET disease is a rare, chronic, multisystem disorder with a variety of symptoms. It most often affects men between the ages of 20 and 40 years. Although it occurs worldwide, it occurs particularly often in Mediterranean countries, the Middle East, and Japan. The etiology of Behcet disease remains obscure. It is considered an autoimmune disease because of the common denominator of vasculitis in most patients. Histologic study of the affected vessels shows leukocytoclastic vasculitis, which leads to thrombosis, obstruction, aneurysm formation, and rupture of vessels. Arteries, capillaries, and veins of various sizes are affected. Behcet aneurysms may involve the whole arterial tree (1). We report a case of arterioportal fistula in a patient with Behcet disease, which resulted from spontaneous rupture of a giant hepatic artery aneurysm into the superior mesenteric vein (SMV).