Caring for Pediatric Patients With Epidermolysis Bullosa in the Emergency Department

被引：3

作者：

Jenkinson, Helena A. ^{[1
]}

Lundgren, Ashley D. ^{[2
,3
]}

Levy, Moise L. ^{[2
,3
,4
]}

Diaz, Lucia Z. ^{[2
,3
,4
]}

机构：

[1] Univ Texas Austin, Dell Med Sch, Dept Internal Med, Austin, TX 78712 USA

[2] Univ Texas Austin, Dell Med Sch, Dept Internal Med Dermatol, Austin, TX 78712 USA

[3] Univ Texas Austin, Dell Med Sch, Dept Pediat Pediat Dermatol, Dell Childrens Med Ctr, Austin, TX 78712 USA

[4] Dell Childrens Med Ctr, Pediat Adolescent Dermatol, Austin, TX USA

来源：

PEDIATRIC EMERGENCY CARE | 2019年 / 35卷 / 08期

关键词：

epidermolysis bullosa; iatrogenic trauma; mucosa; skin; wound care; immunobullous disease; health care delivery; PAIN MANAGEMENT; CHILDREN; ANESTHESIA; MUTATIONS;

D O I：

10.1097/PEC.0000000000001500

中图分类号：

R4 [临床医学];

学科分类号：

1002 ; 100602 ;

摘要：

Epidermolysis bullosa (EB) refers to a heterogeneous group of genetic disorders characterized by epithelial fragility. We provide guidelines for management of pediatric patients with EB in the emergency department based on a review of literature, as well as insights from our own experiences caring for patients with EB. The purpose of the guidelines proposed is prevention of avoidable iatrogenic trauma to the skin and mucosa of patients with EB who are presenting to the emergency department for a variety of reasons.

引用

页码：579 / 584

页数：6

共 17 条

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