Plasma C3d levels as a diagnostic marker for complete complement factor I deficiency

被引:6
作者
Naesens, Leslie [1 ,2 ]
Smet, Julie [5 ]
Tavernier, Simon J. [1 ,6 ]
Schelstraete, Petra [3 ]
Hoste, Levi [1 ,3 ]
Lambrecht, Stijn [4 ]
Verhelst, Helene [7 ]
ten Bosch, Jutte van der Werff [8 ]
Ferster, Alina [9 ]
Blumental, Sophie [9 ]
Hilbert, Pascale [10 ]
Kerre, Tessa [2 ]
Walle, Johan Vande [11 ]
Licht, Christoph [12 ]
Roumenina, Lubka T. [13 ]
Stordeur, Patrick [5 ]
Haerynck, Filomeen [1 ,3 ]
机构
[1] Ghent Univ Hosp, Primary Immunodeficiency Res Lab, Ghent, Belgium
[2] Ghent Univ Hosp, Dept Hematol, Ctr Primary Immunodeficiency Ghent, Jeffrey Modell Diag & Res Ctr, Ghent, Belgium
[3] Ghent Univ Hosp, Dept Pediat, Div Pediat Pulmonol Infect Dis & Immunol, Ghent, Belgium
[4] Ghent Univ Hosp, Div Lab Med, Dept Clin Chem, Ghent, Belgium
[5] Univ Libre Bruxelles, Belgian Natl Reference Ctr Complement Syst, Immunol Lab, LHUB ULB, Brussels, Belgium
[6] VIB Inflammat Res Ctr, Immunoregulat Lab, Ghent, Belgium
[7] Univ Hosp Ghent, Div Pediat Neurol, Dept Pediat, Ghent, Belgium
[8] Univ Ziekenhuis Brussel, Dept Pediat, Div Pediat Oncol & Immunol, Jette, Belgium
[9] Univ Libre Bruxelles, Dept Pediat, Dept Haematol Oncol, Childrens Univ Hosp Queen Fabiola, Brussels, Belgium
[10] Inst Pathol & Genet, Dept Human Genet, Gosselies, Belgium
[11] Univ Hosp Ghent, Div Pediat Nephrol, Dept Pediat, Ghent, Belgium
[12] Hosp Sick Children, Dept Pediat, Div Pediat Nephrol, Toronto, ON, Canada
[13] Univ Paris, Ctr Rech Cordeliers, INSERM, Sorbonne Univ, Paris, France
关键词
MUTATIONS;
D O I
10.1016/j.jaci.2020.08.014
中图分类号
R392 [医学免疫学];
学科分类号
100102 ;
摘要
[No abstract available]
引用
收藏
页码:749 / +
页数:14
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