Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease

被引:1
作者
Maddali, Madan Mohan [1 ]
Junghare, Minakshi Sandip [1 ]
Nishant, Arora Ram [1 ]
Kandachar, Pranav Subbaraya [2 ]
Valliattu, Johan [2 ]
机构
[1] Royal Hosp, Dept Cardiac Anesthesia, Natl Heart Ctr, Muscat, Oman
[2] Royal Hosp, Natl Heart Ctr, Dept Cardiothorac Surg, Muscat, Oman
关键词
FETAL-HEMOGLOBIN; SURGERY; RISK;
D O I
10.1111/jocs.12721
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Hypoxemia is a well-known trigger for precipitating a sickling crisis in patients with sickle cell disease. Patients undergoing staged single ventricle palliation have hypoxemia during the initial stages of the Fontan pathway. The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described. doi: 10.1111/jocs.12721 (J Card Surg 2016;31:237-241)
引用
收藏
页码:237 / 241
页数:5
相关论文
共 50 条
[41]   Palliation Outcomes of Neonates Born With Single-Ventricle Anomalies Associated With Aortic Arch Obstruction [J].
Alsoufi, Bahaaldin ;
McCracken, Courtney ;
Shashidharan, Subhadra ;
Kogon, Brian ;
Border, William ;
Kanter, Kirk .
ANNALS OF THORACIC SURGERY, 2017, 103 (02) :637-644
[42]   Single Ventricle Palliation in a Developing Sub-Saharan African Country: What Should be Improved? [J].
Manuel, Valdano ;
Morais, Humberto ;
Turquetto, Aida L. R. ;
Miguel, Gade ;
Miana, Leonardo A. ;
Pedro, Albino ;
Nunes, Maria A. S. ;
Leon, Gilberto ;
Magalhaes, Manuel Pedro ;
Martins, Telmo ;
Junior, Antonio P. F. .
WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY, 2019, 10 (02) :164-170
[43]   Sickle cell disease biochip: a functional red blood cell adhesion assay for monitoring sickle cell disease [J].
Alapan, Yunus ;
Kim, Ceonne ;
Adhikari, Anima ;
Gray, Kayla E. ;
Gurkan-Cavusoglu, Evren ;
Little, Jane A. ;
Gurkan, Umut A. .
TRANSLATIONAL RESEARCH, 2016, 173 :74-91
[44]   Single nucleotide polymorphisms and sickle cell disease-related pain: a systematic review [J].
Gehling, Gina M. ;
Powell-Roach, Keesha ;
Wilkie, Diana J. ;
Dungan, Jennifer R. .
FRONTIERS IN PAIN RESEARCH, 2023, 4
[45]   Laparoscopic cholecystectomy in 427 adults with sickle cell disease: a single-center experience [J].
Al-Mulhim, Abdulrahman S. ;
Al-Mulhim, Abdulmohsen A. .
SURGICAL ENDOSCOPY AND OTHER INTERVENTIONAL TECHNIQUES, 2009, 23 (07) :1599-1602
[46]   In-vitro and Computational Study of the Assisted Bidirectional Glenn Procedure for Initial Palliation of Single Ventricle Physiology [J].
Esmaily-Moghadam, Mandi ;
Zhou, Jian ;
Hsia, Tain-Yen ;
Figliola, Richard ;
Marsden, Alison .
CIRCULATION, 2014, 130
[47]   Sickle Cell Disease and Elective Cholecystectomy [J].
Leake, P. A. ;
Toppin, Jp ;
King, L. ;
Reid, M. ;
Scotto, P. ;
Duncan, N. D. ;
McFarlane, M. E. C. .
WEST INDIAN MEDICAL JOURNAL, 2019, 68 :3-9
[48]   Gene therapy for sickle cell disease [J].
Olowoyeye, Abiola ;
Okwundu, Charles I. .
COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 2010, (08)
[49]   Hydroxyurea (hydroxycarbamide) for sickle cell disease [J].
Nevitt, Sarah J. ;
Jones, Ashley P. ;
Howard, Jo .
COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 2017, (04)
[50]   Advances in the Treatment of Sickle Cell Disease [J].
Kapoor, Sargam ;
Little, Jane A. ;
Pecker, Lydia H. .
MAYO CLINIC PROCEEDINGS, 2018, 93 (12) :1810-1824