Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease

被引：1
作者：
Maddali, Madan Mohan [1 ]
Junghare, Minakshi Sandip [1 ]
Nishant, Arora Ram [1 ]
Kandachar, Pranav Subbaraya [2 ]
Valliattu, Johan [2 ]
机构：
[1] Royal Hosp, Dept Cardiac Anesthesia, Natl Heart Ctr, Muscat, Oman
[2] Royal Hosp, Natl Heart Ctr, Dept Cardiothorac Surg, Muscat, Oman
来源：
JOURNAL OF CARDIAC SURGERY | 2016年 / 31卷 / 04期
关键词：
FETAL-HEMOGLOBIN; SURGERY; RISK;
D O I：
10.1111/jocs.12721
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Hypoxemia is a well-known trigger for precipitating a sickling crisis in patients with sickle cell disease. Patients undergoing staged single ventricle palliation have hypoxemia during the initial stages of the Fontan pathway. The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described. doi: 10.1111/jocs.12721 (J Card Surg 2016;31:237-241)
引用
收藏
页码：237 / 241
页数：5
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