Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: A case report

被引：5

作者：

Youn, Joong Kee ^{[1
]}

Lee, Jeong-Moo ^{[1
]}

Yi, Nam-Joon ^{[1
]}

Choi, Young Rok ^{[1
]}

Suh, Suk-Won ^{[1
]}

You, Tae ^{[1
]}

Lee, Kwang-Woong ^{[1
]}

Jung, Chul-Woo ^{[2
]}

Lee, Ji-won ^{[2
]}

Bae, Eun-Jung ^{[3
]}

Ko, Jae Sung ^{[3
]}

Kim, Woong-Han ^{[4
]}

Park, Kwi-Won ^{[1
]}

Suh, Kyung-Suk ^{[1
]}

机构：

[1] Seoul Natl Univ, Coll Med, Dept Surg, Seoul 110744, South Korea

[2] Seoul Natl Univ, Coll Med, Dept Anesthisiol & Pain Med, Seoul 110744, South Korea

[3] Seoul Natl Univ, Coll Med, Dept Pediat, Seoul 110744, South Korea

[4] Seoul Natl Univ, Coll Med, Dept Thorac Surg, Seoul 110744, South Korea

来源：

PEDIATRIC TRANSPLANTATION | 2014年 / 18卷 / 08期

关键词：

biliary atresia; left isomerism; Fontan operation; hepatopulmonary syndrome; liver transplantation; SITUS-INVERSUS; HEPATOPULMONARY SYNDROME; OPERATION; MORTALITY; SURGERY; COMPLICATIONS; CIRCULATION; PREDICTORS; OUTCOMES; CHILDREN;

D O I：

10.1111/petr.12364

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA. CHD can be associated with LI in up to 15% of cases, although it is rare in BA. Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three-yr-old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA.

引用

页码：E274 / E279

页数：6

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