carpal tunnel syndrome;
children;
electromyography;
Maroteaux-Lamy disease;
median nerve;
D O I:
10.1159/000065099
中图分类号:
R74 [神经病学与精神病学];
学科分类号:
摘要:
We report a 28-month-old male child, known to have Maroteaux-Lamy syndrome (mucopolysaccharidosis type VI), who presented with inconsistent right hand discomfort. Clinical suspicion of right carpal tunnel syndrome was confirmed by nerve conduction and electromyographic studies, and a decompressive procedure was done with uneventful recovery. Carpal tunnel syndrome in mucopolysaccharidosis patients should be suspected, diagnosed and treated early for better outcome. Copyright (C) 2002 S. KargerAG, Basel.
机构:
Stanford Univ Hosp, Div Emergency Med, Emergency Med Serv, Stanford, CA 94305 USAStanford Univ Hosp, Div Emergency Med, Emergency Med Serv, Stanford, CA 94305 USA
机构:
Louisiana State Univ, Hlth Sci Ctr, Sch Med, Dept Family Med, New Orleans, LA 70112 USALouisiana State Univ, Hlth Sci Ctr, Sch Med, Dept Family Med, New Orleans, LA 70112 USA
LeBlanc, Kim Edward
Cestia, Wayne
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机构:
Louisiana State Univ, Hlth Sci Ctr, Sch Med, Dept Family Med, New Orleans, LA 70112 USALouisiana State Univ, Hlth Sci Ctr, Sch Med, Dept Family Med, New Orleans, LA 70112 USA
机构:
Univ Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, AustraliaUniv Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, Australia
Charles, Janice
Fahridin, Salma
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h-index: 0
机构:
Univ Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, AustraliaUniv Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, Australia
Fahridin, Salma
Britt, Helena
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h-index: 0
机构:
Univ Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, AustraliaUniv Sydney, Australian GP Stat & Classificat Ctr, Sydney, NSW 2006, Australia