carpal tunnel syndrome;
children;
electromyography;
Maroteaux-Lamy disease;
median nerve;
D O I:
10.1159/000065099
中图分类号:
R74 [神经病学与精神病学];
学科分类号:
摘要:
We report a 28-month-old male child, known to have Maroteaux-Lamy syndrome (mucopolysaccharidosis type VI), who presented with inconsistent right hand discomfort. Clinical suspicion of right carpal tunnel syndrome was confirmed by nerve conduction and electromyographic studies, and a decompressive procedure was done with uneventful recovery. Carpal tunnel syndrome in mucopolysaccharidosis patients should be suspected, diagnosed and treated early for better outcome. Copyright (C) 2002 S. KargerAG, Basel.
机构:
Nihon Univ, Sch Med, Dept Pediat Surg, Nerima Hikarigaoka Hosp, Tokyo 1790072, JapanNihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, Japan
Masuko, Takayuki
Fuchigami, Tatsuo
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机构:
Nihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, JapanNihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, Japan
Fuchigami, Tatsuo
Inadomi, Toru
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机构:
Nihon Univ, Sch Med, Dept Dermatol, Nerima Hikarigaoka Hosp, Tokyo 1790072, JapanNihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, Japan
Inadomi, Toru
Inamo, Yasuji
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机构:Nihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, Japan
Inamo, Yasuji
Hashimoto, Koji
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机构:Nihon Univ, Sch Med, Nerima Hikarigaoka Hosp, Dept Gen Pediat,Nerima Ku, Tokyo 1790072, Japan