Behcet's syndrome (BS) is classified as a variable vessel vasculitis. The clinical picture is very diverse and usually requires interdisciplinary collaboration. Pathogenetically, BS seems to take a middle position between a polygenic autoinflammatory disease and an autoimmune disease. New EULAR recommendations were issued in 2018. The therapy depends on which organs are most affected. Since 2016, adalimumab has been approved for the treatment of posterior ocular involvement. Infliximab, interferon a2a, interleukin-1 antagonists and apremilast may be alternative therapies.
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
de Oliveira Ribeiro, Natalia P.
de Mello Schier, Alexandre R.
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
de Mello Schier, Alexandre R.
Pessoa, Tamires M.
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Pessoa, Tamires M.
Pereira, Valeska M.
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Pereira, Valeska M.
Machado, Sergio
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Salgado de Oliveira Univ PPGCAF UNIVERSO, Phys Act Sci Postgrad Program, Phys Act Neurosci Lab LABNAF, Niteroi, RJ, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Machado, Sergio
Arias-Carrion, Oscar
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Secretaria Salud Mexico, Hosp Gen Dr Manuel Gea Gonzalez, Unidad Trastornos Movimiento & Sueno, Mexico City, DF, MexicoFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Arias-Carrion, Oscar
Nardi, Antonio E.
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil
Nardi, Antonio E.
Cardoso, Adriana
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Fed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, BrazilFed Univ Rio de Janeiro IPUB UFRJ, Inst Psychiat, Lab Pan & Respirat, Rio De Janeiro, Brazil