Behcet's Syndrome

被引:0
|
作者
Xenitidis, Theodoros [1 ]
Henes, Joerg Christoph [1 ]
机构
[1] Univ Klinikum Tubingen, Med Univ Klin, Abt & Lehrstuhl 2, Hamatol Onkol Klin Immunol Rheumatol, Tubingen, Germany
关键词
Vasculitis; Review; Therapy; Behcet's syndrome; PULMONARY-ARTERY INVOLVEMENT; INTERFERON ALPHA-2A; DOUBLE-BLIND; GASTROINTESTINAL MANIFESTATIONS; CLINICAL-FEATURES; NERVOUS-SYSTEM; DISEASE; COLCHICINE; UVEITIS; PREVALENCE;
D O I
10.1055/a-0979-4510
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Behcet's syndrome (BS) is classified as a variable vessel vasculitis. The clinical picture is very diverse and usually requires interdisciplinary collaboration. Pathogenetically, BS seems to take a middle position between a polygenic autoinflammatory disease and an autoimmune disease. New EULAR recommendations were issued in 2018. The therapy depends on which organs are most affected. Since 2016, adalimumab has been approved for the treatment of posterior ocular involvement. Infliximab, interferon a2a, interleukin-1 antagonists and apremilast may be alternative therapies.
引用
收藏
页码:262 / 275
页数:14
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