Radiological evaluation, management, and surveillance of renal masses in Von Hippel-Lindau disease

被引:43
|
作者
Meister, M. [1 ]
Choyke, P. [2 ]
Anderson, C. [3 ]
Patel, U. [1 ]
机构
[1] St George Hosp, Dept Radiol, London SW17 0QT, England
[2] St George Hosp, Dept Urol, London SW17 0QT, England
[3] NIH, Dept Radiol, Bethesda, MD 20892 USA
关键词
PARENCHYMAL SPARING SURGERY; BOSNIAK CATEGORY-III; CELL CARCINOMA; VHL GENE; RADIOFREQUENCY ABLATION; PROGNOSTIC-SIGNIFICANCE; IMAGING FEATURES; TUMOR SIZE; CANCER; CT;
D O I
10.1016/j.crad.2008.10.010
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Von Hippel-Lindau disease (VHL) is a rare, autosomal-dominant condition that predisposes patients to developing renal cysts and tumours. VHL is the most common of the hereditary renal cancer syndromes, and is exclusively associated with the clear cell histological subtype of renal cell carcinoma. This review focuses on the genetics, surveillance, and management of complex renal masses in VHL. The current status of renal cyst analysis in general. and in the context of VHL is also reviewed. (C) 2008 The Royal College of Radiologists. Published by Elsevier Ltd. All rights reserved.
引用
收藏
页码:589 / 600
页数:12
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