Von Hippel-Lindau disease (VHL) is a rare, autosomal-dominant condition that predisposes patients to developing renal cysts and tumours. VHL is the most common of the hereditary renal cancer syndromes, and is exclusively associated with the clear cell histological subtype of renal cell carcinoma. This review focuses on the genetics, surveillance, and management of complex renal masses in VHL. The current status of renal cyst analysis in general. and in the context of VHL is also reviewed. (C) 2008 The Royal College of Radiologists. Published by Elsevier Ltd. All rights reserved.
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Montefiore Med Ctr, Dept Surg, 111 East 210th St, Bronx, NY 10467 USA
Albert Einstein Coll Med, 1300 Morris Pk Ave, Bronx, NY 10461 USANCI, Endocrine Oncol Branch, Ctr Canc Res, NIH, Bldg 10,Room 4-5940, Bethesda, MD 20891 USA
Libutti, Steven K.
Jonasch, Eric
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Univ Texas MD Anderson Canc Ctr, Div Canc Med, Dept Genitourinary Med Oncol, 1155 Pressler St,Unit 1374, Houston, TX 77030 USANCI, Endocrine Oncol Branch, Ctr Canc Res, NIH, Bldg 10,Room 4-5940, Bethesda, MD 20891 USA
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Chaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Tel Aviv Univ, Sackler Fac Med, Tel Aviv, IsraelChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Laks, Shachar
van Leeuwaarde, Rachel
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Univ Med Ctr Utrecht, Dept Endocrine Oncol, Utrecht, NetherlandsChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
van Leeuwaarde, Rachel
Patel, Dhaval
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NCI, NIH, Bethesda, MD USAChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Patel, Dhaval
Keutgen, Xavier M.
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Univ Chicago, Med Ctr, Dept Surg, Div Endocrine Surg, Chicago, IL 60637 USAChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Keutgen, Xavier M.
Hammel, Pascal
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Hop Paul Brousse, Dept Digest & Med Oncol, Villejuif, FranceChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Hammel, Pascal
Nilubol, Naris
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NCI, NIH, Bethesda, MD USAChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Nilubol, Naris
Links, Thera P.
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Univ Groningen, Univ Med Ctr Groningen, Dept Internal Med, Div Endocrinol, Groningen, NetherlandsChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Links, Thera P.
Halfdanarson, Thorvardur R.
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Mayo Clin, Div Med Oncol, Ctr Canc, Rochester, MN USAChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Halfdanarson, Thorvardur R.
Daniels, Anthony B.
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Vanderbilt Univ, Div Ocular Oncol & Pathol, Dept Ophthalmol & Visual Sci, Vanderbilt Eye Inst,Med Ctr, Nashville, TN USA
Vanderbilt Univ, Med Ctr, Vanderbilt Ingram Canc Ctr, Nashville, TN USAChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel
Daniels, Anthony B.
Tirosh, Amit
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Tel Aviv Univ, Sackler Fac Med, Tel Aviv, Israel
Chaim Sheba Med Ctr, Neuroendocrine Tumors Serv, VHL Clin Care Ctr, Endocrine Oncol Genom Lab, Tel Hashomer, IsraelChaim Sheba Med Ctr, Surg C, Tel Hashomer, Israel