Persistent Mullerian Duct Syndrome with torsion of an intra-abdominal seminoma

被引：0

作者：

Masereel, B ^{[1
]}

Michiels, G ^{[1
]}

机构：

[1] St Dimpna Ziekenhuis, Dept Surg, Geel, Belgium

来源：

ACTA CHIRURGICA BELGICA | 1999年 / 99卷 / 05期

关键词：

Mullerian ducts; cryptorchidism; pseudohermaphroditism; seminoma;

D O I：

暂无

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Persistent Mullerian Duct Syndrome (PMDS) is a particular form of male pseudohermaphroditism. Due to the absence or inactivity of Mullerian Inhibiting Substance (MIS), no regression is observed of the Mullerian ducts in a genotypical and phenotypical male individual. This leads to the development of fallopian tubes, uterus and proximal vagina. The testes often lie intra-abdominally and are exposed to malignant degeneration. A case is described in which the diagnosis of PMDS was made by laparotomy for an acute abdomen, caused by torsion of a seminoma.

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页码：256 / 259

页数：4

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