Circulating polymers in alpha(1)-antitrypsin deficiency

被引：57

作者：

Tan, Lu ^{[1
]}

Dickens, Jennifer A. ^{[1
]}

DeMeo, Dawn L. ^{[3
,4
]}

Miranda, Elena ^{[15
]}

Perez, Juan ^{[16
]}

Rashid, S. Tamir ^{[1
]}

Day, James ^{[1
]}

Ordonez, Adriana ^{[1
]}

Marciniak, Stefan J. ^{[1
]}

Haq, Imran ^{[1
]}

Barker, Alan F. ^{[5
]}

Campbell, Edward J. ^{[6
,7
]}

Eden, Edward ^{[8
]}

McElvaney, Noel G. ^{[17
]}

Rennard, Stephen I. ^{[9
]}

Sandhaus, Robert A. ^{[10
]}

Stocks, James M. ^{[11
]}

Stoller, James K. ^{[12
]}

Strange, Charlie ^{[13
]}

Turino, Gerard ^{[8
]}

Rouhani, Farshid N. ^{[14
]}

Brantly, Mark ^{[14
]}

Lomas, David A. ^{[2
]}

机构：

[1] Univ Cambridge, Cambridge Inst Med Res, Dept Med, Cambridge CB2 1TN, England

[2] UCL, Div Med, London, England

[3] Brigham & Womens Hosp, Dept Med, Channing Div Network Med, Boston, MA 02115 USA

[4] Brigham & Womens Hosp, Dept Med, Div Pulm & Crit Care Med, Boston, MA 02115 USA

[5] Oregon Hlth & Sci Univ, Sch Med, Dept Med, Portland, OR 97201 USA

[6] Intermt Hlth Care, Provo, UT USA

[7] HerediLab Inc, Salt Lake City, UT USA

[8] St Lukes Roosevelt Hosp, New York, NY 10025 USA

[9] Univ Nebraska, Med Ctr, Dept Pulm & Crit Care Med, Omaha, NE USA

[10] Natl Jewish Hlth, Denver, CO USA

[11] Univ Texas Hlth Ctr Tyler, Tyler, TX USA

[12] Cleveland Clin, Cleveland, OH 44106 USA

[13] Med Univ S Carolina, Coll Med, Dept Med, Charleston, SC 29425 USA

[14] Univ Florida, Coll Med, Dept Med, Gainesville, FL USA

[15] Univ Roma La Sapienza, Cenci Bolognetti Fdn, Inst Pasteur, Dept Biol & Biotechnol Charles Darwin, I-00185 Rome, Italy

[16] Univ Malaga, Dept Cell Biol Genet & Physiol, E-29071 Malaga, Spain

[17] Beaumont Hosp, Dublin 9, Ireland

来源：

EUROPEAN RESPIRATORY JOURNAL | 2014年 / 43卷 / 05期

关键词：

POLYMERIZATION; MECHANISM; LIVER;

D O I：

10.1183/09031936.00111213

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

引用

页码：1501 / 1504

页数：4

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