Dermatofibrosarcoma protuberans: a rare entity and review of the literature

被引：1

作者：

Stamatakos, Michael ^{[1
]}

Fyllos, Apostolos ^{[2
]}

Siafogianni, Alexia ^{[3
]}

Ntzeros, Konstantinos ^{[1
]}

Tasiopoulou, Georgia ^{[2
]}

Rozis, Meletios ^{[1
]}

Kontzoglou, Konstantinos ^{[4
]}

机构：

[1] Gen Hosp Korinthos, Dept Surg, Korinthos, Greece

[2] Gen Hosp Karditsa, Dept Surg, Kardhitsa, Greece

[3] Univ Athens, Andreas Sygros Hosp, Dept Dermatol, Athens, Greece

[4] Hosp Hegau Bodensee Klinikum, Dept Internal Med, Radolfzell am Bodensee, Germany

来源：

JOURNAL OF BUON | 2014年 / 19卷 / 01期

关键词：

dermatofibrosarcoma protuberans; positive margins; radiotherapy; soft tissue tumor; SOFT-TISSUE SARCOMAS; MOHS MICROGRAPHIC SURGERY; IMATINIB MESYLATE; LOCAL RECURRENCE; MANAGEMENT; THERAPY; MARKER;

D O I：

暂无

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Dermatofibrosarcoma protuberans (DFSP) is an uncommon malignant mesenchymal tumor. The incidence of DFSP is 0.1% of all cancers and less than 2% of all soft tissue sarcomas (STS). It can appear at any age, most commonly in individuals aged between 20 and 50 years. The usual location of DFSP is the trunk and it is limited to the dermis. Wide radical excision is the preferred surgical method for therapy of DFSP without distant metastasis. The probability of regional or distant metastases is less than 5%. Patients with positive or close surgical margins have an elevated risk of local recurrence after resection. Adjuvant radiotherapy administered either before or after the surgical treatment reduces the risk of local recurrence.

引用

页码：34 / 41

页数：8

共 45 条

[1] Dermatofibrosarcoma protuberans with fibrosarcomatous transformation of the head and neck [J].