Constriction Band Syndrome

被引:31
作者
Kawamura, Kenji [2 ]
Chung, Kevin C. [1 ]
机构
[1] Univ Michigan, Sch Med, Dept Surg, Sect Plast Surg, Ann Arbor, MI 48109 USA
[2] Nara Med Univ, Dept Orthopaed Surg, Nara 6348522, Japan
关键词
Constriction band syndrome; Malformation; Congenital anomaly; Hand; Treatment; SONOGRAPHIC DIAGNOSIS; MANAGEMENT; DEFECTS; COMPLEX; RINGS; LIMB;
D O I
10.1016/j.hcl.2008.10.007
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
Constriction band syndrome is an uncommon congenital abnormality with multiple disfiguring and disabling manifestations. Early amnion rupture with subsequent entanglement of fetal parts by amniotic strands is currently the primary theory for the development of this syndrome. Management of constriction band syndrome is focused on improving function and development while providing a more acceptable esthetic appearance. The treatment should be tailored to the individual. Timing of repair and surgical planning are important to provide the best functional results for affected hands.
引用
收藏
页码:257 / +
页数:10
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