Living Donor Liver Transplantation for an Infant with Osteogenesis Imperfecta and Intrahepatic Cholestasis: Report of a Case

被引：2

作者：

Choi, YoungRok ^{[1
]}

Yi, Nam-Joon ^{[1
]}

Ko, Jae Sung ^{[2
]}

Ko, Jung Min ^{[2
]}

Jin, Ung Sik ^{[3
]}

Kim, Hee Soo ^{[4
]}

Lee, Kook Hyun ^{[4
]}

Cho, Tae-Joon ^{[5
]}

Suh, Suk-Won ^{[1
]}

Yoo, Tae ^{[1
]}

Lee, Kwang-Woong ^{[1
]}

Suh, Kyung-Suk ^{[1
]}

机构：

[1] Seoul Natl Univ, Coll Med, Dept Surg, Seoul 110744, South Korea

[2] Seoul Natl Univ, Coll Med, Dept Pediat & Adolescent Med, Seoul 110744, South Korea

[3] Seoul Natl Univ, Coll Med, Dept Plast & Reconstruct Surg, Seoul 110744, South Korea

[4] Seoul Natl Univ, Coll Med, Dept Anesthesiol & Pain Med, Seoul 110744, South Korea

[5] Seoul Natl Univ, Coll Med, Dept Orthopaed Surg, Seoul 110744, South Korea

来源：

JOURNAL OF KOREAN MEDICAL SCIENCE | 2014年 / 29卷 / 03期

关键词：

Osteogenesis Imperfecta; Liver Transplantation; Cholestatic Liver Disease; Malignant Hyperthermia; INFUSION; PROPOFOL;

D O I：

10.3346/jkms.2014.29.3.441

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Osteogenesis imperfecta (OI) is a group of genetic disorders characterized by bone fragility and connective tissue manifestations. We report a successful liver transplantation (LT) in an 8-month-old boy with OI and cholestatic biliary cirrhosis. After 4 cycles of intravenous pamidronate, LT was performed under intravenous anesthesia using a left lateral section from his mother without mechanical retractors. The operation time was 420 min and estimated blood loss was 520 mL requiring one unit of RBC transfusion. He was discharged without surgical complications. Therefore, LT should be considered for patients with end stage liver disease and OI under organic multidisciplinary cooperation.

引用

页码：441 / 444

页数：4

共 13 条

[1] Aortic valve replacement in osteogenesis imperfecta - Technical and practical considerations for a successful outcome [J].

Badmanaban, B ;

Sachithanandan, A ;

MacGowan, SW .

JOURNAL OF CARDIAC SURGERY, 2003, 18 (06) :554-556

[2]

Byra P, 2008, AM J MED SCI, V336, P70, DOI 10.1097/MAJ.0b013e318158e981

[3] Short-term efficacy of monthly pamidronate infusion in patients with osteogenesis imperfecta [J].

Choi, Jin-Ho ;

Shin, Young-Lim ;

Yoo, Han-Wook .

JOURNAL OF KOREAN MEDICAL SCIENCE, 2007, 22 (02) :209-212

[4] Osteogenesis imperfecta [J].

Forin, Veronique .

PRESSE MEDICALE, 2007, 36 (12) :1787-1793

[5] Normative Data for Bone Mass in Healthy Term Infants from Birth to 1 Year of Age [J].

Gallo, Sina ;

Vanstone, Catherine A. ;

Weiler, Hope A. .

JOURNAL OF OSTEOPOROSIS, 2012, 2012

[6]

Han EC, 2011, J KOREAN SOC TRANSPL, V25, P276

[7] Outflow vein reconstruction of extended right lobe graft using quilt venoplasty technique [J].

Hwang, S ;

Lee, SG ;

Ahn, CS ;

Moon, DB ;

Kim, KH ;

Ha, TY ;

Song, GW .

LIVER TRANSPLANTATION, 2006, 12 (01) :156-158

[8] Lacticacidosis after short-term infusion of propofol for anaesthesia in a child with osteogenesis imperfecta [J].

Kill, C ;

Leonhardt, A ;

Wulf, H .

PAEDIATRIC ANAESTHESIA, 2003, 13 (09) :823-826

[9] Postnatal development of bone mineral status during infancy [J].

Koo, WWK ;

Bush, AJ ;

Walters, J ;

Carlson, SE .

JOURNAL OF THE AMERICAN COLLEGE OF NUTRITION, 1998, 17 (01) :65-70

[10] Propofol bashing: The time to stop is now! [J].

Reed, MD ;

Blumer, JL .

CRITICAL CARE MEDICINE, 1996, 24 (01) :175-177

← 1 2 →