Coexistence of intracranial arteriovenous malformation with Turcot's syndrome: A case report

被引：1

作者：

Umezawa, K ^{[1
]}

Kumabe, T ^{[1
]}

Shirane, R ^{[1
]}

Yoshimoto, T ^{[1
]}

机构：

[1] Tohoku Univ, Sch Med, Dept Neurosurg, Aoba Ku, Sendai, Miyagi 9808574, Japan

来源：

SURGICAL NEUROLOGY | 1999年 / 52卷 / 04期

关键词：

adenomatous polyposis; arteriovenous malformation; glioma; multiplicity; Turcot's syndrome;

D O I：

10.1016/S0090-3019(99)00099-3

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Turcot's syndrome is a combination of multiple adenomatous gastrointestinal polyps and neuroepithelial tumors of the central nervous system (CNS). A 16-year-old man presented with Turcot's syndrome consisting of nonfamilial colorectal polyposis and multiple fibrillary astrocytomas accompanied by ruptured intracranial arteriovenous malformation (AVM) manifesting as generalized epileptic activity. Multiple CNS tumors are extremely unusual in Turcot's syndrome. This is the first description of Turcot's syndrome associated with an intracranial AVM. This case may correspond to a new phenotypic variant of colonic polyposis syndrome. (C) 1999 by Elsevier Science Inc.

引用

页码：397 / 399

页数：3