Primary Spinal Intradural Extraosseous Ewing Sarcoma in a Pediatric Patient: Case Report and Review of the Literature

被引：13

作者：

Scantland, Joshua T. ^{[1
]}

Gondim, Mercia J. ^{[2
]}

Koivuniemi, Andrew S. ^{[3
]}

Fulkerson, Daniel H. ^{[3
]}

Shih, Chie-Schin ^{[4
]}

机构：

[1] Indiana Univ Sch Med, Indianapolis, IN 46202 USA

[2] Indiana Univ Hlth, Dept Pathol & Lab Med, Indianapolis, IN USA

[3] Indiana Univ Sch Med, Dept Neurol Surg, Goodman Campbell Brain & Spine, Indianapolis, IN 46202 USA

[4] Indiana Univ Hlth, Pediat Oncol & Hematol, Indianapolis, IN USA

来源：

PEDIATRIC NEUROSURGERY | 2018年 / 53卷 / 04期

关键词：

Intradural sarcoma; Intraspinal sarcoma; Extraosseous sarcoma; Ewing sarcoma; Spine; Pediatric surgery; PRIMITIVE NEUROECTODERMAL TUMOR; CAUDA-EQUINA; LUMBAR SPINE;

D O I：

10.1159/000488767

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Ewing sarcoma (ES) is an aggressive, primary bone malignancy with occasional soft tissue extension. Purely extraosseous ES is rare. A primary intraspinal, intradural ES without bone involvement is exceedingly rare. ES may be differentiated from other primitive neuroectodermal tumors by molecular analysis. The authors report the case of a 14-year-old female who suffered an acute neurologic decline from a hemorrhagic, intraspinal, intradural ES. The patient has been tumor free for 2 years after the initial emergency surgery. Our management of the patient and a review of the literature are provided. Considering only those cases with molecular or genetic confirmation of ES, our patient is the fifth pediatric case reported in the English literature. (c) 2018 S. Karger AG, Basel.

引用

页码：222 / 228

页数：7

共 25 条

[1] Intradural Extramedullary Ewing's Sarcoma Recurrence with Acute Clinical Presentation and Literature Review [J].