Sclerosing cholangitis associated with hypereosinophilic syndrome

被引:15
作者
Ichikawa, N
Taniguchi, A
Akama, H
Ishiguro, H
Kurihara, T
Terai, C
Hara, M
Kashiwazaki, S
机构
[1] Department of Rheumatology, Institute of Rheumatology, Tokyo Women's Medical College, Tokyo
[2] Aoyama Hospital, Tokyo Women's Medical College, Tokyo
[3] Department of Rheumatology, Institute of Rheumatology, Tokyo Women's Medical College, Shinjuku-ku, Tokyo 162, Wakamatsu-cho
关键词
eosinophilia; endoscopic retrograde cholangiopancreatography (ERCP); corticosteroid; ursodeoxycholic acid (UDCA);
D O I
10.2169/internalmedicine.36.561
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 15-year-old male with hypereosinophilic syndrome was admitted to our hospital because of general malaise and abnormal liver function tests. Endoscopic retrograde cholangiopancreatography demonstrated bile duct changes consistent with primary sclerosing cholangitis. The patient's liver profile tests returned to normal after treatment with prednisolone and ursodeoxycholic acid. In this case, eosinophils might have played an important role in the pathogenesis of the bile duct lesion.
引用
收藏
页码:561 / 564
页数:4
相关论文
共 12 条
[1]   THE IDIOPATHIC HYPEREOSINOPHILIC SYNDROME - CLINICAL, PATHOPHYSIOLOGIC, AND THERAPEUTIC CONSIDERATIONS [J].
FAUCI, AS ;
HARLEY, JB ;
ROBERTS, WC ;
FERRANS, VJ ;
GRALNICK, HR ;
BJORNSON, BH .
ANNALS OF INTERNAL MEDICINE, 1982, 97 (01) :78-92
[2]  
FOONG A, 1991, HEPATOLOGY, V13, P1090, DOI 10.1002/hep.1840130614
[3]  
GRAUER L, 1993, AM J GASTROENTEROL, V88, P1764
[4]   CONJUGATES OF URSODEOXYCHOLATE PROTECT AGAINST CYTOTOXICITY OF MORE HYDROPHOBIC BILE-SALTS - INVITRO STUDIES IN RAT HEPATOCYTES AND HUMAN ERYTHROCYTES [J].
HEUMAN, DM ;
PANDAK, WM ;
HYLEMON, PB ;
VLAHCEVIC, ZR .
HEPATOLOGY, 1991, 14 (05) :920-926
[5]  
KAGAWA K, 1988, SOGORINSHO, V37, P2339
[6]   PRIMARY SCLEROSING CHOLANGITIS [J].
LEE, YM ;
KAPLAN, MM .
NEW ENGLAND JOURNAL OF MEDICINE, 1995, 332 (14) :924-933
[7]  
MIRMADJLESSI SH, 1986, AM J GASTROENTEROL, V81, P483
[8]   MARKED EOSINOPHILIA IN A PATIENT WITH PRIMARY SCLEROSING CHOLANGITIS [J].
NEEMAN, A ;
KADISH, U .
AMERICAN JOURNAL OF MEDICINE, 1987, 83 (02) :378-379
[9]   HYPEREOSINOPHILIC SYNDROME RESEMBLING CHRONIC INFLAMMATORY BOWEL-DISEASE WITH PRIMARY SCLEROSING CHOLANGITIS [J].
SCHEURLEN, M ;
MORK, H ;
WEBER, P .
JOURNAL OF CLINICAL GASTROENTEROLOGY, 1992, 14 (01) :59-63
[10]   EOSINOPHILIC GASTROENTERITIS PRESENTING WITH COLITIS AND CHOLANGITIS [J].
SCHOONBROODT, D ;
HORSMANS, Y ;
LAKA, A ;
GEUBEL, AP ;
HOANG, P .
DIGESTIVE DISEASES AND SCIENCES, 1995, 40 (02) :308-314