Thrombotic microangiopathy with ANCA-associated vasculitis in a child: a case report and review of literature

被引:0
作者
Zhang, Rui [1 ]
Zhou, Jia-Fan [1 ]
Liang, Meng-Jun [1 ]
Huang, Ya-Juan [1 ]
Li, Ai-Hua [1 ]
Su, Ning [1 ]
Huang, Miao-Fang [1 ]
Zhang, Qian-Hui [1 ]
Jiang, Zong-Pei [1 ]
机构
[1] Sun Yat Sen Univ, Affiliated Hosp 6, Dept Nephrol, 26 Yuancun Erheng Rd, Guangzhou 510655, Guangdong, Peoples R China
来源
INTERNATIONAL JOURNAL OF CLINICAL AND EXPERIMENTAL PATHOLOGY | 2017年 / 10卷 / 02期
关键词
Thrombotic mircroangiopathy; ANCA-related vasculitis; HENOCH-SCHONLEIN PURPURA; HEMOLYTIC-UREMIC SYNDROME; HYPOCOMPLEMENTEMIA; GLOMERULONEPHRITIS; OUTCOMES;
D O I
暂无
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We describe a case with acute renal failure, pulmonary bleeding, rashes and abdominal pain in a 9-year-old girl suffered from Thrombotic mircroangiopathy (TMA). The reason of TMA was ANCA-related vasculitis, which was seldom seen in pediatric patients. This type of patient is easily misdiagnosed as henoch-schoenlein purpura. The patient was given prednisone and mycophenolate mofetil (MMF) for the treatment of ANCA-related vasculitis. The renal function returned to normal and proteinuria decreased dramatically.
引用
收藏
页码:2255 / 2258
页数:4
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