A case of eosinophilic fasciitis without skin manifestations: a case report in a patient with lupus and literature review

被引：3

作者：

Asaoka, Kohei ^{[1
]}

Watanabe, Yuki ^{[1
]}

Itoh, Kazuhiro ^{[2
,3
,4
]}

Hosono, Naoko ^{[2
]}

Hirota, Tomoya ^{[2
]}

Ikawa, Masamichi ^{[5
]}

Yamaguchi, Tomohisa ^{[5
]}

Hatta, Satomi ^{[6
]}

Imamura, Yoshiaki ^{[6
]}

Nishino, Ichizo ^{[7
]}

Yamauchi, Takahiro ^{[2
]}

Iwasaki, Hiromichi ^{[2
,4
]}

机构：

[1] Univ Fukui, Fac Med Sci, Fukui, Japan

[2] Univ Fukui, Dept Internal Med 1, Fac Med Sci, 23-3 Matsuokashimoaizuki, Fukui 9101193, Japan

[3] Natl Hosp Org Awara Hosp, Dept Internal Med, Awara, Japan

[4] Univ Fukui Hosp, Dept Infect Control & Prevent, Fukui, Japan

[5] Univ Fukui, Dept Internal Med 2, Fac Med Sci, Fukui, Japan

[6] Univ Fukui Hosp, Div Surg Pathol, Fukui, Japan

[7] Natl Ctr Neurol & Psychiat, Natl Inst Neurosci, Dept Neuromuscular Res, Tokyo, Japan

来源：

CLINICAL RHEUMATOLOGY | 2021年 / 40卷 / 06期

关键词：

Eosinophilic fasciitis; Diagnostic criteria; Skin manifestations; Systemic lupus erythematosus; SHULMAN DISEASE; ERYTHEMATOSUS; DIAGNOSIS; CHILD;

D O I：

10.1007/s10067-020-05416-6

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Eosinophilic fasciitis (EF) is a rare connective tissue disease that causes inflammation and fibrosis of the fascia, inducing pain and motor dysfunction. Characteristic skin manifestations, such as edema, erythema, induration, peau d'orange appearance, and the groove sign, are of diagnostic significance and observed in the majority of patients with EF. We herein report a case of EF without these characteristic skin manifestations. A 66-year-old Japanese woman developed progressive limb pain and motor dysfunction. No skin changes were observed. We diagnosed the patient with EF based on the clinical course, magnetic resonance imaging, and en bloc biopsy containing fascia and muscle. Oral prednisolone therapy markedly attenuated limb pain and motor dysfunctions. Through a systemic search of the medical literature, we retrieved 4 juvenile cases and 8 adult cases of EF without characteristic skin manifestations during the clinical course. We herein present a systemic review on EF without skin manifestations and discuss differences between the two proposed sets of diagnostic criteria of EF.

引用

页码：2477 / 2483

页数：7

共 31 条

[1]

Aringer M, 2019, ARTHRITIS RHEUMATOL, V71, P1400, DOI [10.1002/art.40930, 10.1136/annrheumdis-2018-214819]

[2] SYSTEMIC LUPUS-ERYTHEMATOSUS AND EOSINOPHILIC FASCIITIS - AN UNUSUAL ASSOCIATION [J].