Familial hemophagocytic lymphohistiocytosis

被引：1
作者：
Raka, S. [1 ]
Nayar, P. [1 ]
Godbole, R. [1 ]
Manchanda, R. [1 ]
机构：
[1] King Edward Mem Hosp, Dept Pathol, Pune, Maharashtra, India
来源：
INDIAN JOURNAL OF HEMATOLOGY AND BLOOD TRANSFUSION | 2009年 / 25卷 / 02期
关键词：
Bone marrow; Cytopenia; Ferritin;
D O I：
10.1007/s12288-009-0018-2
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
A 45-day-old infant presented with hepatosplenomegaly and fever since 15 days. Hemogram revealed bicytopenia and bone marrow aspirate showed hemophagocytosis. With the history of death of two siblings, the baby was diagnosed with hemophagocytic lymphohistiocytosis (HLH), likely to be of familial origin.
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页码：78 / 80
页数：3
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