The Role of Trichoscopy in Keratosis Follicularis Spinulosa Decalvans: Case Report and Review of the Literature

被引:7
|
作者
Alessandrini, Aurora [1 ]
Brattoli, Giancarlo [2 ]
Piraccini, Bianca Maria [1 ]
Di Altobrando, Ambra [1 ]
Starace, Michela [1 ]
机构
[1] Univ Bologna, Dermatol, Dept Expt Diagnost & Specialty Med DIMES, Bologna, Italy
[2] Univ Padua, Dept Med DIMED, Dermatol Unit, Padua, Italy
来源
SKIN APPENDAGE DISORDERS | 2021年 / 7卷 / 01期
关键词
Keratosis follicularis spinulosa decalvans; Scarring alopecia; Trichoscopy; Pathology; ICHTHYOSIS FOLLICULARIS; ALOPECIA; PILARIS; THERAPY; FAILURE; LINKAGE;
D O I
10.1159/000510525
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Introduction: Keratosis follicularis spinulosa decalvans (KFSD) is a rare, X-linked, hereditary disorder of keratinization, characterized by skin involvement and progressive scarring alopecia of scalp, eyebrows, and eyelashes. The diagnosis is helped by the particular clinical features, but pathology is mandatory. Case Presentation: We described a case of a female patient referred to the outpatient's hair consultation of our department, in which we performed trichoscopy as a very useful tool for the diagnosis, followed by pathology that confirmed KFSD. Conclusion: In our article, we underlined the importance of trichoscopy for the diagnosis of this hair disease, with also a review of the literature on diagnosis and treatment.
引用
收藏
页码:29 / 35
页数:7
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