A rare case of internal jugular vein aneurysm with massive hemorrhage in neurofibromatosis type 1

被引：9

作者：

Hiraki, Tsubasa ^{[1
]}

Higashi, Michiyo ^{[1
]}

Goto, Yuko ^{[1
]}

Kitazono, Ikumi ^{[1
]}

Yokoyama, Seiya ^{[1
]}

Iuchi, Hiroyuki ^{[3
]}

Nagano, Hiromi ^{[3
]}

Tanimoto, Akihide ^{[2
]}

Yonezawa, Suguru ^{[1
]}

机构：

[1] Kagoshima Univ, Grad Sch Med & Dent Sci, Field Oncol, Dept Human Pathol, Kagoshima 890, Japan

[2] Kagoshima Univ, Grad Sch Med & Dent Sci, Field Oncol, Kagoshima 890, Japan

[3] Kagoshima Univ, Grad Sch Med & Dent Sci, Dept Otolaryngol Head & Neck Surg, Kagoshima 890, Japan

来源：

CARDIOVASCULAR PATHOLOGY | 2014年 / 23卷 / 04期

关键词：

Neurofibromatosis; NF1; Internal jugular vein aneurysm; Fatal hemorrhage; Venous aneurysm;

D O I：

10.1016/j.carpath.2014.02.001

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Neurofibromatosis Type 1 (NF1) is a relatively common autosomal dominant disorder. Vascular involvement is a well-recognized manifestation of NF1, but venous aneurysm associated with NF1 is extremely rare. We present a case of an NF1 patient with a left internal jugular vein aneurysm with massive hemorrhage occurring during surgery. Due to the extreme fragility of both the aneurismal wall and the surrounding tissue, the patient developed severe intraoperative bleeding. Pathological examination confirmed aneurismal wall infiltration of the neurofibromatosis. Physicians should be aware that hemorrhagic complication in NF1 can occur and be fatal. (C) 2014 The Authors. Published by Elsevier Inc.

引用

页码：244 / 247

页数：4

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