An Atypical Case of Poland Syndrome with Bilateral Features and Dextroposition of the Heart
被引:3
作者:
Geeroms, Barbara
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机构:
UZ Leuven, Leuven, BelgiumUZ Leuven, Leuven, Belgium
Geeroms, Barbara
[1
]
Breysem, Luc
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h-index: 0
机构:
UZ Leuven, Leuven, BelgiumUZ Leuven, Leuven, Belgium
Breysem, Luc
[1
]
Aertsen, Michael
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h-index: 0
机构:
UZ Leuven, Leuven, BelgiumUZ Leuven, Leuven, Belgium
Aertsen, Michael
[1
]
机构:
[1] UZ Leuven, Leuven, Belgium
来源:
JOURNAL OF THE BELGIAN SOCIETY OF RADIOLOGY
|
2019年
/
103卷
/
01期
关键词:
Case report;
Poland syndrome;
dextrocardia;
chest wall;
chest deformity;
D O I:
10.5334/jbsr.1860
中图分类号:
R8 [特种医学];
R445 [影像诊断学];
学科分类号:
1002 ;
100207 ;
1009 ;
摘要:
Poland syndrome is defined by the unilateral aplasia or hypoplasia of the sternocostal head of the major pectoral muscle and is associated with variable ipsilateral thoracic and upper limb anomalies. Most frequently, the abnormalities are unilateral and on the right side. We present an atypical case of Poland syndrome in a baby girl with bilateral chest abnormalities, mainly on the left side, and secondary dextroposition of the heart. As required in almost all cases of Poland syndrome, different imaging modalities were used to evaluate the extent of our patient's anomalies.
机构:
Comenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Cingel, Vladimir
Bohac, Martin
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机构:
Comenius Univ, Dept Plast Surg, Fac Med, Univ Hosp, Bratislava 82606, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Bohac, Martin
Mestanova, Veronika
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h-index: 0
机构:
Comenius Univ, Inst Histol & Embryol, Jessenius Fac Med, Martin 03601, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Mestanova, Veronika
Zabojnikova, Lenka
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h-index: 0
机构:
Comenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Zabojnikova, Lenka
Varga, Ivan
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h-index: 0
机构:
Comenius Univ, Inst Histol & Embryol, Fac Med, Bratislava 81108, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
机构:
Comenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Cingel, Vladimir
Bohac, Martin
论文数: 0引用数: 0
h-index: 0
机构:
Comenius Univ, Dept Plast Surg, Fac Med, Univ Hosp, Bratislava 82606, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Bohac, Martin
Mestanova, Veronika
论文数: 0引用数: 0
h-index: 0
机构:
Comenius Univ, Inst Histol & Embryol, Jessenius Fac Med, Martin 03601, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Mestanova, Veronika
Zabojnikova, Lenka
论文数: 0引用数: 0
h-index: 0
机构:
Comenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia
Zabojnikova, Lenka
Varga, Ivan
论文数: 0引用数: 0
h-index: 0
机构:
Comenius Univ, Inst Histol & Embryol, Fac Med, Bratislava 81108, SlovakiaComenius Univ, Dept Pediat Surg, Fac Med, Childrens Med Hosp, Bratislava 83340, Slovakia