The Currarino triad: Its importance in pediatric neurosurgery

Currarino's triad is a hereditary condition diagnosed when three abnormalities are noted: (1) an anorectal malformation; (2) an anterior sacral defect, and (3) a presacral mass. This condition often presents with symptoms related to the presacral mass or with an incidental finding of a sacral anomaly on plain radiographs. Presented here are 2 cases of Currarino's triad noted in siblings, both of whom underwent surgery for anorectal malformations in infancy. The importance of early diagnosis and treatment of this condition and the need for genetic counseling are emphasized.